Pentalogy of Cantrell with Total Ectopia Cordis and a Major Omphalocele—A Case Report
- Arturo Leonardo Delgado, Kopolo Mfuneko Matongo, Bangasa Dumo, Ntsikelelo Mzayiya, Busisiwe Mrara
- Authors: Arturo Leonardo Delgado , Kopolo Mfuneko Matongo , Bangasa Dumo , Ntsikelelo Mzayiya , Busisiwe Mrara
- Date: 2019
- Language: English
- Type: Journal
- Identifier: http://hdl.handle.net/11260/5079 , vital:44343
- Full Text:
- Authors: Arturo Leonardo Delgado , Kopolo Mfuneko Matongo , Bangasa Dumo , Ntsikelelo Mzayiya , Busisiwe Mrara
- Date: 2019
- Language: English
- Type: Journal
- Identifier: http://hdl.handle.net/11260/5079 , vital:44343
- Full Text:
Pentalogy of Cantrell with Total Ectopia Cordis and a Major Omphalocele—A Case Report
- Delgado, Arturo Leonardo, Matongo, Kopolo Mfuneko, Dumo, Bangasa, Mzayiya, Ntsikelelo, Mrara, Busisiwe
- Authors: Delgado, Arturo Leonardo , Matongo, Kopolo Mfuneko , Dumo, Bangasa , Mzayiya, Ntsikelelo , Mrara, Busisiwe
- Date: 2019
- Subjects: Ectopia cordis, major omphalocele, sternum agenesis, anterior diaphragmatic deficiency, absence of pericardium, persistence of the Ductus arteriosus.
- Language: English
- Type: Journal Article
- Identifier: http://hdl.handle.net/11260/6360 , vital:45379
- Description: Abstract: Ectopia cordis (EC) is a rare malformation due to failure of maturation of the midline mesodermal components of the chest and abdomen. It can be defined as 0.1% of congenital heart diseases, and it could present isolated or could belong to the spectrum of the Pentalogy of Cantrell (PoC), which is a rare congenital disorder first described in 1958 by Cantrell.We are reporting a rare case of total ectopia cordis, associated to a major omphalocele, total agenesis of the sternum, anterior diaphragmatic deficiency, absence of pericardium, and persistence of the Ductus arteriosus, making therefore these features compatible with a full spectrum of the Pentalogy of Cantrell, encouraging us to report this case.
- Full Text:
- Authors: Delgado, Arturo Leonardo , Matongo, Kopolo Mfuneko , Dumo, Bangasa , Mzayiya, Ntsikelelo , Mrara, Busisiwe
- Date: 2019
- Subjects: Ectopia cordis, major omphalocele, sternum agenesis, anterior diaphragmatic deficiency, absence of pericardium, persistence of the Ductus arteriosus.
- Language: English
- Type: Journal Article
- Identifier: http://hdl.handle.net/11260/6360 , vital:45379
- Description: Abstract: Ectopia cordis (EC) is a rare malformation due to failure of maturation of the midline mesodermal components of the chest and abdomen. It can be defined as 0.1% of congenital heart diseases, and it could present isolated or could belong to the spectrum of the Pentalogy of Cantrell (PoC), which is a rare congenital disorder first described in 1958 by Cantrell.We are reporting a rare case of total ectopia cordis, associated to a major omphalocele, total agenesis of the sternum, anterior diaphragmatic deficiency, absence of pericardium, and persistence of the Ductus arteriosus, making therefore these features compatible with a full spectrum of the Pentalogy of Cantrell, encouraging us to report this case.
- Full Text:
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